Idiopathic orbital inflammatory syndrome: a dermatological perspective

Idiopathic orbital inflammatory syndrome: a dermatological perspective: Priyanka Sharma, Jasleen Kaur, Rakesh Kumar Bansal, Gurvinder P Thami



Egyptian Journal of Dermatology and Venerology 2020 40(1):59-61



Idiopathic orbital inflammatory syndrome, formerly known as orbital pseudotumor, is a rare benign condition with myriad clinical presentations including periorbital edema, pain, conjunctival chemosis, diplopia, extraocular muscle restriction, and decreased vision. It is a relatively lesser known clinical entity from a dermatological perspective and may present as recurrent periorbital edema as a sole manifestation as in this case, and thus can potentially be mistaken for angioedema. The objective of this case report is to emphasize on the wide range of clinical manifestations and the need for awareness of this entity and thus avoiding its misdiagnosis.