Κυριακή 8 Μαρτίου 2020


Does facility volume influence survival in patients with primary malignant bone tumors of the vertebral column? A comparative cohort study.
Related ArticlesDoes facility volume influence survival in patients with primary malignant bone tumors of the vertebral column? A comparative cohort study. Spine J. 2020 Mar 04;: Authors: Lazarides AL, Kerr DL, Dial B, Steele JR, Lane WO, Blazer DG, Brigman BE, Mendoza-Lattes S, Erickson ME, Eward WC Abstract BACKGROUND CONTEXT: Facility volume has been correlated with survival in many cancers. This relationship has not been established in primary malignant...
Rare Cancers
Sun Mar 08, 2020 13:50
Sickle cell disease induces resistance to cutaneous carcinogenesis.
Related ArticlesSickle cell disease induces resistance to cutaneous carcinogenesis. Orphanet J Rare Dis. 2020 Mar 06;15(1):66 Authors: Soutou B, Senet P, Lionnet F, Habibi A, Aractingi S Abstract BACKGROUND: While skin carcinomas are reported in chronic ulcers and in patients treated with hydroxyurea (HU) for myeloproliferative neoplasms, no skin carcinoma has been reported in patients with sickle cell disease (SCD), presenting chronic skin ulcers or...
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Sun Mar 08, 2020 12:21
TLD1433 Photosensitizer Inhibits Conjunctival Melanoma Cells in Zebrafish Ectopic and Orthotopic Tumour Models.
Related ArticlesTLD1433 Photosensitizer Inhibits Conjunctival Melanoma Cells in Zebrafish Ectopic and Orthotopic Tumour Models. Cancers (Basel). 2020 Mar 04;12(3): Authors: Chen Q, Ramu V, Aydar Y, Groenewoud A, Zhou XQ, Jager MJ, Cole H, Cameron CG, McFarland SA, Bonnet S, Snaar-Jagalska BE Abstract The ruthenium-based photosensitizer (PS) TLD1433 has completed a phase I clinical trial for photodynamic therapy (PDT) treatment of bladder cancer. Here,...
Rare Cancers
Sun Mar 08, 2020 12:21
Rare Histological Variants of Prostate Adenocarcinoma: A National Cancer Database Analysis.
Related ArticlesRare Histological Variants of Prostate Adenocarcinoma: A National Cancer Database Analysis. J Urol. 2020 Mar 06;:101097JU0000000000001011 Authors: Bronkema C, Arora S, Sood A, Dalela D, Keeley J, Borchert A, Baumgarten L, Rogers CG, Peabody JO, Menon M, Abdollah F Abstract PURPOSE: The American Joint Committee on Cancer recognizes six rare histological variants of prostate adenocarcinoma. Our aim was to describe the contemporary presentation...
Rare Cancers
Sat Mar 07, 2020 14:46
Clinical response to pazopanib in a patient with endolymphatic sac tumor not associated with von Hippel-Lindau syndrome.
Related ArticlesClinical response to pazopanib in a patient with endolymphatic sac tumor not associated with von Hippel-Lindau syndrome. CNS Oncol. 2020 Mar 06;:CNS50 Authors: Nelson T, Hu J, Bannykh S, Fan X, Rudnick J, Vail E Abstract Endolymphatic sac tumors (ELSTs) are rare, locally invasive, vascular tumors of the temporal bone. These lesions are associated with von Hippel-Lindau syndrome but may arise sporadically. Early surgical intervention is...
Rare Cancers
Sat Mar 07, 2020 14:46
Prevalence of CD8+ cytotoxic lymphocytes in human neoplasms.
Related ArticlesPrevalence of CD8+ cytotoxic lymphocytes in human neoplasms. Cell Oncol (Dordr). 2020 Mar 05;: Authors: Blessin NC, Spriestersbach P, Li W, Mandelkow T, Dum D, Simon R, Hube-Magg C, Lutz F, Viehweger F, Lennartz M, Fraune C, Nickelsen V, Fehrle W, Göbel C, Weidemann S, Clauditz T, Lebok P, Möller K, Steurer S, Izbicki JR, Sauter G, Minner S, Jacobsen F, Luebke AM, Büscheck F, Höflmayer D, Wilczak W, Burandt E, Hinsch A Abstract PURPOSE:...
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Sat Mar 07, 2020 13:14
Unexpected Histopathological Diagnosis of Undifferentiated Uterine Sarcoma after Simple Hysterectomy: Extrapolating Limited Evidence.
Related ArticlesUnexpected Histopathological Diagnosis of Undifferentiated Uterine Sarcoma after Simple Hysterectomy: Extrapolating Limited Evidence. Cureus. 2020 Jan 27;12(1):e6783 Authors: Davis AA Abstract Uterine sarcomas are a rare malignancy, often retrospectively diagnosed after myomectomy or hysterectomy. Undifferentiated uterine sarcomas (UUS) are a particularly aggressive variant of this condition. Little evidence exists regarding the postoperative...
Rare Cancers
Sat Mar 07, 2020 13:14
Gastric Cardia Adenocarcinoma with Metastasis to the Scalp: A Case Report.
Related ArticlesGastric Cardia Adenocarcinoma with Metastasis to the Scalp: A Case Report. Cureus. 2020 Jan 27;12(1):e6781 Authors: Menghani SV, Barbosa A, Sagerman P, Beal MW, Scott A Abstract Cutaneous metastasis is a rare manifestation of advanced gastrointestinal (GI) cancers. Gastric adenocarcinoma rarely presents with cutaneous metastasis, as cutaneous manifestations occur in less than 1% of upper GI tract malignancies. Here, we present the case...
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Sat Mar 07, 2020 13:14
Endobronchial Glomus Tumor in a Child.
Related ArticlesEndobronchial Glomus Tumor in a Child. Pediatr Allergy Immunol Pulmonol. 2019 Dec 01;32(4):163-166 Authors: Prero MY, Gener M, Taboada EM, Oermann CM Abstract Glomus tumors (GTs) are rare, usually benign, mesenchymal neoplasms typically located in the cutaneous tissues of the extremities. Visceral locations have been reported in â¼5% of cases. The average age at diagnosis is 42 years. GTs originating in the respiratory tract of pediatric...
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Sat Mar 07, 2020 13:14
Malignant transformation in a Breast Adenomyoepithelioma Caused by Amplification of c-MYC: A Common pathway to Cancer in a Rare Entity.
Related ArticlesMalignant transformation in a Breast Adenomyoepithelioma Caused by Amplification of c-MYC: A Common pathway to Cancer in a Rare Entity. J Breast Cancer. 2020 Feb;23(1):93-99 Authors: Febres-Aldana CA, Mejia-Mejia O, Krishnamurthy K, Mesko T, Poppiti R Abstract Breast adenomyoepitheliomas are composed of a biphasic proliferation of myoepithelial cells around small epithelial-lined spaces. Due to the rarity of adenomyoepitheliomas, the...
Rare Cancers
Sat Mar 07, 2020 13:14
An intracranial mass causing tumor-induced osteomalacia (TIO): Rapid and complete resolution of severe osteoporosis after surgical resection.
Related ArticlesAn intracranial mass causing tumor-induced osteomalacia (TIO): Rapid and complete resolution of severe osteoporosis after surgical resection. Radiol Case Rep. 2020 May;15(5):492-497 Authors: Colazo JM, Thompson RC, Covington NV, Dahir KM Abstract Tumor-induced osteomalacia (TIO) is a rare disease in which patients suffer from fractures and progressive disabling bone pain and muscle weakness. TIO is caused by the hypersecretion of Fibroblast...
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Sat Mar 07, 2020 13:14
Clinical Presentation and Surgical Management of Neonatal Tumors: Retrospective Analysis.
Related ArticlesClinical Presentation and Surgical Management of Neonatal Tumors: Retrospective Analysis. J Indian Assoc Pediatr Surg. 2020 Mar-Apr;25(2):85-90 Authors: Solanki S, Menon P, Samujh R, Gupta K, Rao KLN Abstract Aims: Neonatal tumors (NTs) include a group of diverse neoplasms. In this study, we reviewed our data for clinical presentations, management options, and outcome. Materials and Methods: All patients from 0- to 1-month age...
Rare Cancers
Sat Mar 07, 2020 13:14
Report from the 21st meeting of the European Society of Gynaecological Oncology (ESGO 2019).
Related ArticlesReport from the 21st meeting of the European Society of Gynaecological Oncology (ESGO 2019). Int J Gynecol Cancer. 2020 Mar 05;: Authors: Bizzarri N, Razumova Z, Selcuk I, Taumberger N, Nikolova T, Fotopoulou C, Van der Steen-Banasik E, Ferrero A, Zalewski K Abstract This is a report from the 21st Meeting of the European Society of Gynaecological Oncology (ESGO 2019) held in Athens, Greece, November 2-5, 2019. The conference offered state...
Rare Cancers
Sat Mar 07, 2020 13:14
Epigenetic modulations and lineage plasticity in advanced prostate cancer.
Related ArticlesEpigenetic modulations and lineage plasticity in advanced prostate cancer. Ann Oncol. 2020 Feb 13;: Authors: Ge R, Wang Z, Montironi R, Jiang Z, Cheng M, Santoni M, Huang K, Massari F, Lu X, Cimadamore A, Lopez-Beltran A, Cheng L Abstract Prostate cancer is the most common cancer and second leading cause of cancer-related death in American men. Antiandrogen therapies are part of the standard of therapeutic regimen for advanced or metastatic...
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Sat Mar 07, 2020 13:14
Pan Aurora Kinase Inhibitor: A Promising Targeted-Therapy in Dedifferentiated Liposarcomas With Differential Efficiency Depending on Sarcoma Molecular Profile.
Related ArticlesPan Aurora Kinase Inhibitor: A Promising Targeted-Therapy in Dedifferentiated Liposarcomas With Differential Efficiency Depending on Sarcoma Molecular Profile. Cancers (Basel). 2020 Mar 03;12(3): Authors: Mattei JC, Bouvier-Labit C, Barets D, Macagno N, Chocry M, Chibon F, Morando P, Rochwerger RA, Duffaud F, Olschwang S, Salas S, Jiguet-Jiglaire C Abstract Soft tissue sarcoma (STS) are rare and aggressive tumours. Their classification...
Rare Cancers
Sat Mar 07, 2020 13:14
A case report of sinusoidal diffuse large B-cell lymphoma in a STK4 deficient patient.
Related ArticlesA case report of sinusoidal diffuse large B-cell lymphoma in a STK4 deficient patient. Medicine (Baltimore). 2020 Feb;99(9):e18601 Authors: Ashrafi F, Klein C, Poorpooneh M, Sherkat R, Khoshnevisan R Abstract INTRODUCTION: Primary immunodeficiency diseases (PIDs), a rare group of gene defects with different manifestations, are at great risk of malignancy. The incidence of diffuse large B-cell lymphoma in the sinusoidal tract is quite...
Rare Cancers
Sat Mar 07, 2020 13:14
[Diffuse malignant peritoneal mesothelioma (DMPM) - a rare diagnosis].
Related Articles[Diffuse malignant peritoneal mesothelioma (DMPM) - a rare diagnosis]. Z Gastroenterol. 2020 Feb;58(2):146-151 Authors: Habbel VSA, Mahler EA, Feyerabend B, Oldhafer KJ, Lipp MJ Abstract Diffuse malignant peritoneal mesothelioma (DMPM) is a rare diagnosis, found more frequently in men than in women. Symptoms are unspecific abdominal disorders making that diagnosis difficult to set. Causes of DMPM are yet to be discovered in entirety....
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Sat Mar 07, 2020 13:14
Efficacy and safety of modified endoscopic mucosal resection for rectal neuroendocrine tumors: a meta-analysis.
Related ArticlesEfficacy and safety of modified endoscopic mucosal resection for rectal neuroendocrine tumors: a meta-analysis. Z Gastroenterol. 2020 Feb;58(2):137-145 Authors: Zheng JC, Zheng K, Zhao S, Wang ZN, Xu HM, Jiang CG Abstract PURPOSE: âRectal neuroendocrine tumors are rare with good prognosis. Several endoscopic methods such as endoscopic polypectomy, endoscopic submucosal dissection (ESD), endoscopic mucosal resection (EMR), and modified...
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Sat Mar 07, 2020 13:14
[Klippel-Trenaunay-Weber syndrome with vesical and uterine involvement treated by endoscopic and endovascular routes].
Related Articles[Klippel-Trenaunay-Weber syndrome with vesical and uterine involvement treated by endoscopic and endovascular routes]. Medicina (B Aires). 2020;80(1):84-86 Authors: Rodriguez Peña M, Ovando E Abstract Klippel-Trenaunay-Weber syndrome (KTWS) is a rare venous malformation that generally affects the lower limbs and, more infrequently, the upper limbs. It is characterized by cutaneous angiomatous formations, varicose veins and hypertrophy...
Rare Cancers
Sat Mar 07, 2020 13:14
[Ewing sarcoma of the bone. Multidisciplinary approach and oncological results in 88 patients].
Related Articles[Ewing sarcoma of the bone. Multidisciplinary approach and oncological results in 88 patients]. Medicina (B Aires). 2020;80(1):23-30 Authors: Sanchez-Saba JE, Abrego MO, Albergo JI, Farfalli GL, Aponte-Tinao LA, Ayerza MA, Cayol F, Streitenberger P, Risk MR, Roitman PD Abstract Ewing sarcoma of the bone is a rare, highly aggressive tumor that typically affects children and young adults. In Argentina, the lack of Ewing's sarcoma registries...
Rare Cancers
Sat Mar 07, 2020 13:14
Incidence, treatment and outcome of abdominal metastases in extremity soft tissue sarcoma: Results from a multi-centre study.
Related ArticlesIncidence, treatment and outcome of abdominal metastases in extremity soft tissue sarcoma: Results from a multi-centre study. J Surg Oncol. 2020 Mar;121(4):605-611 Authors: Smolle MA, Schaffler A, Leithner A, Van Praag VM, Bergovec M, Szkandera J, Liegl-Atzwanger B, Niethard M, Tunn PU, Van De Sande M, Andreou D Abstract BACKGROUND AND OBJECTIVES: Abdominal metastases (AM) from soft tissue sarcoma (STS) are rare and prognosis is poor....
Rare Cancers
Sat Mar 07, 2020 13:14
MANAGEMENT OF ENDOCRINE DISEASE: Cushing's syndrome due to ectopic ACTH secretion: an expert operational opinion.
Related ArticlesMANAGEMENT OF ENDOCRINE DISEASE: Cushing's syndrome due to ectopic ACTH secretion: an expert operational opinion. Eur J Endocrinol. 2020 Apr;182(4):R29-R58 Authors: Young J, Haissaguerre M, Viera-Pinto O, Chabre O, Baudin E, Tabarin A Abstract Ectopic ACTH syndrome (EAS) is rare but is frequently a severe condition because of the intensity of the hypercortisolism that may be dissociated from the tumoral condition. EAS should often be...
Rare Cancers
Sat Mar 07, 2020 13:14
Parapharyngeal Alveolar Soft Part Sarcoma in a 5-Year-Old Child.
Related ArticlesParapharyngeal Alveolar Soft Part Sarcoma in a 5-Year-Old Child. J Craniofac Surg. 2020 Jan/Feb;31(1):e99-e101 Authors: Hakeem AH, Patel BK, Swain M, Javaid H Abstract Alveolar soft part sarcoma (ASPS) is a rare malignancy of head and neck region; orbit and tongue being most common subsites affected by this rare tumor. A 5-year-old female presented with computed tomography scan evidence of right-sided prestyloid parapharyngeal mass....
Rare Cancers
Sat Mar 07, 2020 13:14
BURKITT LYMPHOMA IN GASTROINTESTINAL TRACT: A REPORT OF TWO CASES.
Related ArticlesBURKITT LYMPHOMA IN GASTROINTESTINAL TRACT: A REPORT OF TWO CASES. Acta Clin Croat. 2019 Jun;58(2):386-390 Authors: ÄubraniÄ A, GolÄiÄ M, FuÄkar-ÄupiÄ D, BrozoviÄ B, Gajski D, Brumini I Abstract Burkitt lymphoma, a type of non-Hodgkin B-cell lymphoma, is the fastest growing human cancer, presenting pathologically with a 'starry sky' pattern. It is most often found in the abdomen and the jaw, however, localization in the abdomen other...
Rare Cancers
Sat Mar 07, 2020 13:14
Adult Atypical Teratoid/Rhabdoid Tumor in the Pineal Region: Case Report and Literature Review.
Related ArticlesAdult Atypical Teratoid/Rhabdoid Tumor in the Pineal Region: Case Report and Literature Review. World Neurosurg. 2020 Feb;134:428-433 Authors: Monteiro J, Santiago B, Manilha R, Viegas C, Oliveira A, Cunha E Sá M Abstract BACKGROUND: Atypical teratoid/rhabdoid tumor (AT/RT) is a malignant embryonal central nervous system tumor with a poor prognosis. Its occurrence in the pineal region is extremely rare, with only 6 cases in adults reported...
Rare Cancers
Sat Mar 07, 2020 13:14
Spinal Intradural Extramedullary Dermoid Cyst.
Related ArticlesSpinal Intradural Extramedullary Dermoid Cyst. World Neurosurg. 2020 Feb;134:448-451 Authors: Khalighinejad F, Hajizadeh M, Mokhtari A, Rakhshan R, Hajizadeh M, Rezvani M Abstract BACKGROUND: Dermoid cysts are benign congenital tumors that develop early in life. These tumors are classified by the presence of all 3 germ layers. Spinal intradural extramedullary teratoma is a rare disease, which is more common in children under 5 years...
Rare Cancers
Sat Mar 07, 2020 13:14
Cauda Equina Syndrome Secondary to Diffuse Infiltration of the Cauda Equina by Acute Myeloid Leukemia: Case Report and Literature Review.
Related ArticlesCauda Equina Syndrome Secondary to Diffuse Infiltration of the Cauda Equina by Acute Myeloid Leukemia: Case Report and Literature Review. World Neurosurg. 2020 Feb;134:439-442 Authors: Walton A, Mecklosky J, Carr C, Scullen T, Mathkour M, Werner C, Amenta PS Abstract BACKGROUND: Cauda equina syndrome (CES) results from the dysfunction of the lumbar, sacral, and coccygeal rootlets composing the cauda equina. The underlying etiology is...
Rare Cancers
Sat Mar 07, 2020 13:14
Diagnostic Dilemma in Discriminating Between Spinal Neurenteric Cysts and Simple Arachnoid Cysts Based on Embryogenesis and Surgical Correlation.
Related ArticlesDiagnostic Dilemma in Discriminating Between Spinal Neurenteric Cysts and Simple Arachnoid Cysts Based on Embryogenesis and Surgical Correlation. World Neurosurg. 2020 Feb;134:489-494 Authors: Chiang LJ, Wang CK, Tsai HW, Lee JS Abstract BACKGROUND: Neurenteric cyst (NEC) is a rare intradural spinal tumor, but a correct preoperative diagnosis remains challenging. A misdiagnosis of arachnoid cyst (AC) often leads to conflicting surgical...
Rare Cancers
Sat Mar 07, 2020 13:14
Mechanisms and clinical course of cardiovascular toxicity of cancer treatment I. Oncology.
Related ArticlesMechanisms and clinical course of cardiovascular toxicity of cancer treatment I. Oncology. Semin Oncol. 2019 12;46(6):397-402 Authors: Yeh ETH, Ewer MS, Moslehi J, Dlugosz-Danecka M, Banchs J, Chang HM, Minotti G Abstract The opening session of Second International Colloquium on Cardio-Oncology addressed two areas of vital interest. The first reviewed new thoughts related to established agents. While anthracycline cardiotoxicity has...
Rare Cancers
Sat Mar 07, 2020 13:14
Development of a biomarker of efficacy in second-line treatment for lymphangioma of the tongue: a pilot study.
Related ArticlesDevelopment of a biomarker of efficacy in second-line treatment for lymphangioma of the tongue: a pilot study. Br J Oral Maxillofac Surg. 2019 12;57(10):1137-1142 Authors: Pandey V, Tiwari P, Sharma SP, Kumar R, Panigrahi P, Singh OP, Patne S Abstract Lymphangioma of the tongue is a rare lymphatic malformation, and various authors have reported the successful use of sirolimus for its treatment. However, the safety of sirolimus in children...
Rare Cancers
Sat Mar 07, 2020 13:14
Cerebellar Arteriovenous Malformation with Coexistent Hemangioblastoma.
Related ArticlesCerebellar Arteriovenous Malformation with Coexistent Hemangioblastoma. World Neurosurg. 2020 Feb;134:495-500 Authors: Monserrate Marrero JA, Monserrate Marrero AE, Pérez Berenguer JL, Ãlvarez EL, Corona JM, Feliciano C Abstract BACKGROUND: This is a case of a man aged 40 years with a past medical history of smoking, hypertension, polycythemia vera, intellectual disability, and schizophrenia who presented with generalized headaches,...
Rare Cancers
Sat Mar 07, 2020 13:14
Rare NF1 Gene Mutation in Chinese Patient with Neurofibromatosis Type 1 and Anaplastic Astrocytoma.
Related ArticlesRare NF1 Gene Mutation in Chinese Patient with Neurofibromatosis Type 1 and Anaplastic Astrocytoma. World Neurosurg. 2020 Feb;134:434-437 Authors: Zhou S, Zhu Y, Xu J, Tao R, Yuan S Abstract BACKGROUND: Neurofibromatosis type 1 (NF1), a dysregulated neurocutaneous disorder, is an autosomal dominant genetic disease caused by mutations in the NF1 gene. Anaplastic astrocytoma is rare in NF1 patients, and research has proposed that high-grade...
Rare Cancers
Sat Mar 07, 2020 13:14
Small cell carcinoma of the bladder: the characteristics of molecular alterations, treatment, and follow-up.
Related ArticlesSmall cell carcinoma of the bladder: the characteristics of molecular alterations, treatment, and follow-up. Med Oncol. 2019 Oct 29;36(12):98 Authors: Wang Y, Li Q, Wang J, Tong M, Xing H, Xue Y, Pan H, Huang C, Li D Abstract Small cell carcinoma of the bladder (SCCB) is a rare disease associated with high invasiveness and mortality. Histologically, SCCB is difficult to distinguish from small cell lung cancer (SCLC); however, it shares...
Rare Cancers
Sat Mar 07, 2020 13:14
Orbital metastases of invasive lobular breast carcinoma.
Related ArticlesOrbital metastases of invasive lobular breast carcinoma. Breast Dis. 2019;38(3-4):85-91 Authors: Tsagkaraki IM, Kourouniotis CD, Gomatou GL, Syrigos NK, Kotteas EA Abstract Breast cancer is the main site of origin of orbital metastatic disease. Although invasive lobular breast carcinoma accounts for 10-15% of all breast cancer cases, it has been noticed that it metastasizes to the orbit more often compared to breast cancer of no special...
Rare Cancers
Sat Mar 07, 2020 13:14
Primary multifocal anaplastic large cell lymphoma with eyelid involvement: a case report.
Related ArticlesPrimary multifocal anaplastic large cell lymphoma with eyelid involvement: a case report. Arq Bras Oftalmol. 2019;82(6):514-516 Authors: Gargallo-Benedicto A, Bayo-Calduch P, Olate-Pérez Ã, Pérez-Mestre D, Duch-Samper A Abstract Ocular adnexal involvement in CD30+ lymphoproliferative disorders is rare. We report the case of a 73-year-old woman with a relapsing primary cutaneous anaplastic large cell lymphoma on her eyelid. A systemic...
Rare Cancers
Sat Mar 07, 2020 13:14
Glioblastoma in adults with neurofibromatosis type I: A report of two cases.
Related ArticlesGlioblastoma in adults with neurofibromatosis type I: A report of two cases. Neuropathology. 2019 Oct;39(5):368-373 Authors: Narasimhaiah D, Sridutt BS, Thomas B, Vilanilam GC Abstract Neurofibromatosis type I (NF1) is a familial tumor syndrome with an autosomal-dominant inheritance. NF1-associated tumors often include neurofibromas, malignant peripheral nerve sheath tumors and pilocytic astrocytomas of the optic nerve. The presentation...
Rare Cancers
Sat Mar 07, 2020 13:14
A case of recurrent epilepsy-associated rosette-forming glioneuronal tumor with anaplastic transformation in the absence of therapy.
Related ArticlesA case of recurrent epilepsy-associated rosette-forming glioneuronal tumor with anaplastic transformation in the absence of therapy. Neuropathology. 2019 Oct;39(5):389-393 Authors: Halfpenny A, Ferris SP, Grafe M, Woltjer R, Selden N, Nazemi K, Perry A, Solomon DA, Gultekin SH, Moore S, Olson S, Lawce H, Lucas L, Corless CL, Wood MD Abstract Rosette-forming glioneuronal tumor (RGNT) most commonly occurs adjacent to the fourth ventricle...
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Sat Mar 07, 2020 13:14
Polyomaviruses shedding in stool of patients with hematological disorders: detection analysis and study of the non-coding control region's genetic variability.
Related ArticlesPolyomaviruses shedding in stool of patients with hematological disorders: detection analysis and study of the non-coding control region's genetic variability. Med Microbiol Immunol. 2019 Dec;208(6):845-854 Authors: Prezioso C, Ciotti M, Obregon F, Ambroselli D, Rodio DM, Cudillo L, Gaziev J, Mele A, Nardi A, Favalli C, Arcese W, Palamara AT, Pietropaolo V Abstract Fragmented data are available on the human polyomaviruses (HPyVs) prevalence...
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Sat Mar 07, 2020 13:14
Saksenaea infection masquerading as a brain tumor in an immunocompetent child.
Related ArticlesSaksenaea infection masquerading as a brain tumor in an immunocompetent child. Neuropathology. 2019 Oct;39(5):382-388 Authors: Magaki S, Minasian T, Bork J, Harder SL, Deisch JK Abstract Saksenaea species are a rare cause of mucormycosis, the majority associated with cutaneous and subcutaneous infections resulting from trauma in both immunocompromised and immunocompetent individuals. Unlike other causative agents of mucormycosis, cerebral...
Rare Cancers
Sat Mar 07, 2020 13:14
Saprochaete clavata infections in patients undergoing treatment for haematological malignancies: A report of a monocentric outbreak and review of the literature.
Related ArticlesSaprochaete clavata infections in patients undergoing treatment for haematological malignancies: A report of a monocentric outbreak and review of the literature. Mycoses. 2019 Dec;62(12):1100-1107 Authors: Stanzani M, Cricca M, Sassi C, Sutto E, De Cicco G, Bonifazi F, Bertuzzi C, Bacci F, Paolini S, Cavo M, Lewis RE Abstract Saprochaete clavata is a rare cause of fungaemia with deep organ involvement in patients with haematological...
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Sat Mar 07, 2020 13:14
Classic bladder exstrophy and adenocarcinoma of the bladder: Methylome analysis provide no evidence for underlying disease-mechanisms of this association.
Related ArticlesClassic bladder exstrophy and adenocarcinoma of the bladder: Methylome analysis provide no evidence for underlying disease-mechanisms of this association. Cancer Genet. 2019 06;235-236:18-20 Authors: Sharma A, Fröhlich H, Zhang R, Ebert AK, Rösch W, Reis H, Kristiansen G, Ellinger J, Reutter H Abstract The bladder exstrophy-epispadias complex (BEEC) represents the severe end of uro-rectal malformation spectrum involving aberrant embryonic...
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Sat Mar 07, 2020 13:14
Acute lymphoblastic leukemia in a nine-year-old girl with isodicentric chromosome 15 syndrome.
Related ArticlesAcute lymphoblastic leukemia in a nine-year-old girl with isodicentric chromosome 15 syndrome. Cancer Genet. 2019 06;235-236:93-94 Authors: Antonucci R, Vacca N, Ghisu E, Acquaviva G, Cosmi C, Marinaro AM, Locci C, Fozza C Abstract Isodicentric chromosome 15, also called idic(15), is a rare chromosomal abnormality resulting from inverted duplication of proximal 15q. It is associated with specific clinical findings such as early central...
Rare Cancers
Sat Mar 07, 2020 13:14
Laparoscopic management of a low-lying tailgut cyst: a rare case.
Related ArticlesLaparoscopic management of a low-lying tailgut cyst: a rare case. J Obstet Gynaecol. 2019 Nov;39(8):1181-1183 Authors: Aydin Y, Tokgöz VY, Basgun N, Erdemir R PMID: 31064225 [PubMed - indexed for MEDLINE]
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Sat Mar 07, 2020 13:14
Delayed IL-21 treatment preferentially expands peptide-specific CD8+ T cells by reducing bystander activation of T cells.
Related ArticlesDelayed IL-21 treatment preferentially expands peptide-specific CD8+ T cells by reducing bystander activation of T cells. Immunotherapy. 2019 04;11(6):497-513 Authors: Kim SH, Park SY, Lim MC, Lee ES, Lee EG, Han SE, Kim YH, Kwon BS, Choi BK Abstract AIM: We previously reported a simple and practical procedure to generate peptide-specific CD8+ T cells using peptide and IL-2, which is applied to produce human telomerase reverse transcriptase...
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Sat Mar 07, 2020 13:14
Lateral rectus dermoid cyst presenting as incomitant esotropia.
Related ArticlesLateral rectus dermoid cyst presenting as incomitant esotropia. Orbit. 2019 Dec;38(6):507-510 Authors: Koka K, Barh A, Mukherjee B Abstract A 24-year-old male presented with decreased vision associated with inward deviation of his left eye since childhood and gradually progressive prominence of left eye for 6 months. Left eye examination revealed visual acuity of 2/60, convergent squint with restricted abduction and medial dystopia....
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Sat Mar 07, 2020 13:14
Type A lymphomatoid papulosis presenting as an eyelid ulcer in a young man.
Related ArticlesType A lymphomatoid papulosis presenting as an eyelid ulcer in a young man. Orbit. 2019 Dec;38(6):495-499 Authors: Sánchez España JC, Secondi R Abstract We present the case of an ulcerative lesion of the eyelid as first presentation of type A lymphomatoid papulosis (LP) in a young adult. LP is a rare cutaneous lymphoproliferative disease with a risk of associated systemic or cutaneous lymphoma.PMID: 30644803 [PubMed - indexed for MEDLINE]
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Sat Mar 07, 2020 13:14
Odontogenic choristoma presenting as dermolipoma.
Related ArticlesOdontogenic choristoma presenting as dermolipoma. Orbit. 2019 Dec;38(6):492-494 Authors: Men CJ, Wu F, Lee BW, Lin JH, Korn BS, Kikkawa DO Abstract A 5-year-old otherwise healthy girl presented to the oculoplastic service with a painless superotemporal subconjunctival mass in the left eye. Visual acuity was within normal limits, and there was no evidence of proptosis or orbital enlargement. Excision was performed to remove the anterior...
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Sat Mar 07, 2020 13:14
Atypical Squamous Cells of Undetermined Significance Cervical Cytology Report Rate and Histologic Follow-up Findings From the Largest College of American Pathologists-Certified Laboratory in China.
Related ArticlesAtypical Squamous Cells of Undetermined Significance Cervical Cytology Report Rate and Histologic Follow-up Findings From the Largest College of American Pathologists-Certified Laboratory in China. Arch Pathol Lab Med. 2019 06;143(6):748-752 Authors: Zheng B, Yang H, Li Z, You J, Wei G, Zhang H, Zeng Z, Xie F, Zhao C Abstract CONTEXT.—: Reports for atypical squamous cells of undetermined significance (ASC-US) and histologic findings...
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Sat Mar 07, 2020 13:14
Sino-orbital desmoid tumor in a pediatric patient - Case report with review of literature.
Related ArticlesSino-orbital desmoid tumor in a pediatric patient - Case report with review of literature. Orbit. 2019 Dec;38(6):477-485 Authors: Parulan MA, Sundar G, Ong YK, Yeo TT, Lee V, Kimpo MS Abstract We report a case of a 2-year-old female who presented with bilateral progressive proptosis, visual loss, nasal obstruction, and breathing difficulty. Magnetic resonance imaging revealed a large sino-orbital mass that was extending to the orbital...
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Sat Mar 07, 2020 13:14
Pseudomyogenic Hemangioendothelioma.
Related ArticlesPseudomyogenic Hemangioendothelioma. Arch Pathol Lab Med. 2019 06;143(6):763-767 Authors: Al-Qaderi A, Mansour AT Abstract First described in 2003 as epithelioid-sarcoma-like hemangioendothelioma and later in 2011 as pseudomyogenic hemangioendothelioma, this rare vascular tumor is of intermediate malignant potential. It was officially included for the first time in the most recent World Health Organization's Classification of Tumours...
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Sat Mar 07, 2020 13:14
Paraneoplastic syndrome - a rare but treatable cause of non-thyroid-related extraocular muscle enlargement.
Related ArticlesParaneoplastic syndrome - a rare but treatable cause of non-thyroid-related extraocular muscle enlargement. Orbit. 2019 Dec;38(6):468-473 Authors: Kumar S, Diamond T Abstract Paraneoplastic syndrome is a rare but reversible cause of non-thyroid-related extraocular muscle enlargement. We present a 71-year-old lady with diplopia, restricted eye movements, suppressed thyroid-stimulating hormone and enlargement of all extraocular muscles...
Rare Cancers
Sat Mar 07, 2020 13:14
Stent grafts in patients with carotid blowout syndrome: Outcome and antiplatelet therapy in preventive versus emergency cases.
Related ArticlesStent grafts in patients with carotid blowout syndrome: Outcome and antiplatelet therapy in preventive versus emergency cases. Head Neck. 2018 11;40(11):2521-2527 Authors: Kreiser K, Gröber I, Zimmer C, Storck K Abstract BACKGROUND: Carotid blowout syndrome due to tumor infiltration, fistulas, and therapy-related necrosis can occur as late as years after the treatment. Reporting our experiences with preventive and acute treatment with...
Rare Cancers
Sat Mar 07, 2020 13:14
Lingual lymph nodes in patients with squamous cell carcinoma of the tongue and the floor of the mouth.
Related ArticlesLingual lymph nodes in patients with squamous cell carcinoma of the tongue and the floor of the mouth. Head Neck. 2018 11;40(11):2383-2388 Authors: Jia J, Jia MQ, Zou HX Abstract BACKGROUND: The treatment failure for oral squamous cell carcinoma (SCC) frequently takes the form of local and regional recurrences. We investigated the role of lingual lymph nodes (LLNs) in the recurrence of SCC of the tongue and the floor of the mouth. ...
Rare Cancers
Sat Mar 07, 2020 13:14
The current markers of cancer stem cell in oral cancers.
Related ArticlesThe current markers of cancer stem cell in oral cancers. Life Sci. 2020 Mar 02;:117483 Authors: Tahmasebi E, Alikhani M, Yazdanian A, Yazdanian M, Tebyanian H, Seifalian A Abstract Head and neck cancer (HNC) constitute 5% of all reported cancers. Among all, the oral cavity cancer is the most frequent type of HNC which accounts for over half of HNC cases. Mouth cancer ranks the sixth leading cause of cancer-related mortality. Generally,...
Rare Cancers
Fri Mar 06, 2020 22:10
Pediatric myelofibrosis: WHO 2024 update on myeloproliferative neoplasms calling?
Related ArticlesPediatric myelofibrosis: WHO 2024 update on myeloproliferative neoplasms calling? Pediatr Blood Cancer. 2020 Mar 05;:e28232 Authors: Mishra P, Halder R, Aggarwal M, Seth T, Mahapatra M, Pati HP, Saxena R, Tyagi S Abstract OBJECTIVES: Pediatric myelofibrosis is a rare entity with the largest reported series of 19 cases. We describe here the clinicopathological spectrum and outcomes of 15 cases of pediatric myelofibrosis. METHODS:...
Rare Cancers
Fri Mar 06, 2020 22:10
Oesophageal and proximal gastric adenocarcinomas are rare after detection of Helicobacter pylori infection.
Related ArticlesOesophageal and proximal gastric adenocarcinomas are rare after detection of Helicobacter pylori infection. Aliment Pharmacol Ther. 2020 Mar 04;: Authors: Kumar S, Metz DC, Ginsberg GG, Kaplan DE, Goldberg DS Abstract BACKGROUND: Helicobacter pylori infection is the most important risk factor for non-proximal gastric adenocarcinoma, yet some posit it is protective against oesophageal adenocarcinoma and proximal gastric cancers. ...
Rare Cancers
Sat Mar 07, 2020 13:14
Disseminated peritoneal leiomyomatosis: an unusual presentation of intra-abdominal lesion mimicking disseminated malignancy.
Related ArticlesDisseminated peritoneal leiomyomatosis: an unusual presentation of intra-abdominal lesion mimicking disseminated malignancy. Med Pharm Rep. 2020 Jan;93(1):113-116 Authors: Soni S, Pareek P, Narayan S Abstract Leiomyoma are commonly seen as benign smooth muscle tumors of the uterus. Smooth muscle tumors with unusual growth pattern are rare and include 3 primary neoplasms: intravenous leiomyomatosis (IVL), benign metastasizing leiomyoma...
Rare Cancers
Fri Mar 06, 2020 22:10
A Mesothelial Inclusion Cyst Presenting in a 40-Year-Old Woman as Abdominal Pain and Bloating - A Rare Diagnosis.
Related ArticlesA Mesothelial Inclusion Cyst Presenting in a 40-Year-Old Woman as Abdominal Pain and Bloating - A Rare Diagnosis. Eur J Case Rep Intern Med. 2020;7(2):001415 Authors: Canadas S, Fernandes R, Almeida H, Correia JS Abstract Cystic mesotheliomas (also called mesothelial inclusion cysts) are rare benign neoplasms that occur more often in young women. Symptoms are usually non-specific, demanding a thorough work-up. We report a case of a 40-year-old...
Rare Cancers
Fri Mar 06, 2020 22:10
Panitumumab-Induced Eruptive Seborrhoeic Keratosis in a Patient with Metastatic Colorectal Cancer.
Related ArticlesPanitumumab-Induced Eruptive Seborrhoeic Keratosis in a Patient with Metastatic Colorectal Cancer. Eur J Case Rep Intern Med. 2020;7(2):001411 Authors: Koumaki D, Boumpoucheropoulos S, Koumaki V, Katoulis A, Pappas G, Mantaka A, Krasagakis K Abstract Objectives: Agents targeting the epidermal growth factor receptor (EGFR)-mediated signalling pathway are increasingly being used for the treatment of advanced lung, pancreatic, colorectal...
Rare Cancers
Fri Mar 06, 2020 22:10
Angiosarcomaafteradjuvantradiotherapy in high-risksquamouscell carcinoma of the vulva: a case report.
Related ArticlesAngiosarcomaafteradjuvantradiotherapy in high-risksquamouscell carcinoma of the vulva: a case report. Prz Menopauzalny. 2019 Dec;18(4):230-232 Authors: Laliscia C, Gadducci A, Pollina LE, Paiar F Abstract Squamous cell carcinoma of the vulva represents 3-5% of gynecological cancers. The incidence is higher in postmenopausal patients; the mean age of women with vulvar cancer is between 64 and 70 years. Radiotherapy plays an increasing...
Rare Cancers
Fri Mar 06, 2020 22:10
BRCA2 genemutation, c.2808_2811delACAA (p.Ala938Profs), in malebreastcancer - clinicopathologicalanalysisbased on a case report.
Related ArticlesBRCA2 genemutation, c.2808_2811delACAA (p.Ala938Profs), in malebreastcancer - clinicopathologicalanalysisbased on a case report. Prz Menopauzalny. 2019 Dec;18(4):227-229 Authors: Huszno J, Fiszer-Kierzkowska A, PigÅowski W, Mazur M Abstract Male breast cancer (MBC) is a rare disease that occurs in ~0.2% of all neoplasms among men. The risk of developing MBC is higher in men with a BRCA2 genetic mutation (7%). The aim of this study was...
Rare Cancers
Sat Mar 07, 2020 13:14
Recurrent Uterine Smooth-Muscle Tumors of Uncertain Malignant Potential (STUMP): State of The Art.
Related ArticlesRecurrent Uterine Smooth-Muscle Tumors of Uncertain Malignant Potential (STUMP): State of The Art. Anticancer Res. 2020 Mar;40(3):1229-1238 Authors: Rizzo A, Ricci AD, Saponara M, DE Leo A, Perrone AM, DE Iaco P, Pantaleo MA, Nannini M Abstract The term 'uterine STUMP' (smooth-muscle tumors of uncertain malignant potential) is currently used to define a heterogeneous group of uterine tumors distinct from leiomyomas and leiomyosarcomas....
Rare Cancers
Fri Mar 06, 2020 22:10
The French national network dedicated to rare gynecological cancers diagnosis and management could improve the quality of surgery in daily practice of granulosa cell tumors. A TMRG and GINECO group Study.
Related ArticlesThe French national network dedicated to rare gynecological cancers diagnosis and management could improve the quality of surgery in daily practice of granulosa cell tumors. A TMRG and GINECO group Study. Gynecol Oncol. 2020 Mar 01;: Authors: Lenck C, Chopin N, Gouy S, Bonsang-Kitzis H, Martinez-Gomez C, Radosevic-Robin N, Martin S, Lefeuvre-Plesse C, Lambaudie E, Leblanc E, Guyon F, Classe JM, Ramanah R, Beurrier F, Angeles MA, Pomel C, Joly F, de la...
Rare Cancers
Sat Mar 07, 2020 13:14
NUDT7 Loss Promotes KrasG12D CRC Development.
Related ArticlesNUDT7 Loss Promotes KrasG12D CRC Development. Cancers (Basel). 2020 Mar 02;12(3): Authors: Song J, Park S, Oh J, Kim D, Ryu JH, Park WC, Baek IJ, Cheng X, Lu X, Jin EJ Abstract Studies have suggested that dysregulation of peroxisomal lipid metabolism might play an important role in colorectal cancer (CRC) development. Here, we found that KrasG12D-driven CRC tumors demonstrate dysfunctional peroxisomal b-oxidation and identified Nudt7...
Rare Cancers
Sat Mar 07, 2020 13:14
Clinical and morphological correlations and histopathology of joint damage in patients with diffuse-type tenosynovial giant cell tumor.
Related ArticlesClinical and morphological correlations and histopathology of joint damage in patients with diffuse-type tenosynovial giant cell tumor. Wiad Lek. 2019;72(12 cz 1):2269-2276 Authors: Dyadyk OO, Hryhorovska AV Abstract OBJECTIVE: Introduction: Tenosynovial giant cell tumor (TSGCT) (synonym - pigmented villonodular synovitis) - is a rare benign proliferative lesion of the synovial sheath, localized in the joint capsule, bursa or tendon sheath...
Rare Cancers
Sat Mar 07, 2020 13:14
[Clinical features of 54 cases of lung adenocarcinomas with c-ROS oncogene 1 fusion].
Related Articles[Clinical features of 54 cases of lung adenocarcinomas with c-ROS oncogene 1 fusion]. Zhonghua Jie He He Hu Xi Za Zhi. 2020 Feb 12;43(2):120-125 Authors: Cao H, Zheng J, Zhao J, Guo XJ, Zhou JY, Ding W, Zhou JY Abstract Objective: To study the prevalence of c-ros oncogene 1 fusion in lung adenocarcinoma and to evaluate its relationship with clinical characteristics. Methods: We retrospectively analyzed epidermal growth factor receptor...
Rare Cancers
Sat Mar 07, 2020 13:14
[Characterization of different renal cell carcinoma entities].
Related Articles[Characterization of different renal cell carcinoma entities]. Urologe A. 2020 Feb;59(2):135-141 Authors: Rupp NJ, Moch H Abstract BACKGROUND: In recent years, the characterization of different renal cell carcinoma entities has significantly improved, in particular due to molecular typing. OBJECTIVES: Classical, accepted and emerging renal cell carcinoma entities are described. MATERIALS AND METHODS: A literature search...
Rare Cancers
Sat Mar 07, 2020 13:14
A Case of Infratentorial Meningioma Causing Spontaneous Downbeat Nystagmus: Case Report and Review of the Literature.
Related ArticlesA Case of Infratentorial Meningioma Causing Spontaneous Downbeat Nystagmus: Case Report and Review of the Literature. World Neurosurg. 2020 Feb;134:577-579 Authors: Kuwano A, Arai K, Aihara Y, Kawamata T Abstract BACKGROUND: Spontaneous downbeat nystagmus is a finding that raises suspicions of a central nervous system disorder. Vermis and lower brainstem lesions are considered to be responsible, but the exact mechanism is still controversial....
Rare Cancers
Fri Mar 06, 2020 22:10
Thoracic Intradural Extramedullary Ependymoma with Anaplastic Transformation: Case Report and Discussion.
Related ArticlesThoracic Intradural Extramedullary Ependymoma with Anaplastic Transformation: Case Report and Discussion. World Neurosurg. 2020 Feb;134:549-554 Authors: Akhunbay-Fudge CY, Chakrabarty A, Derham C, Pal D Abstract BACKGROUND: Intradural extramedullary spinal ependymomas arising from outside the region of the conus medullaris are rare clinical entities, and anaplastic transformation of these lesions is even more exceptional. CASE...
Rare Cancers
Fri Mar 06, 2020 22:10
Intraspinal Canal Schwannoma with Extensive Calcification: Case Report and Literature Review.
Related ArticlesIntraspinal Canal Schwannoma with Extensive Calcification: Case Report and Literature Review. World Neurosurg. 2020 Feb;134:555-559 Authors: Zhong B, Shao Z, Pan H Abstract BACKGROUND: Schwannomas are the most common benign tumors in the intraspinal location, with slow-growing and nonaggressive features. Calcification is not a common histopathological and radiological feature in schwannoma. CASE DESCRIPTION: We report the case...
Rare Cancers
Fri Mar 06, 2020 22:10
Contralateral Sudden Sensorineural Hearing Loss After Vestibular Schwannoma Surgery.
Related ArticlesContralateral Sudden Sensorineural Hearing Loss After Vestibular Schwannoma Surgery. World Neurosurg. 2020 Feb;134:564-568 Authors: Wang Y Abstract BACKGROUND: Contralateral sudden sensorineural hearing loss (SNHL) after vestibular schwannoma (VS) surgery is extremely rare, and the mechanism of hearing loss remains unclear. This report aims to provide details of a new case of contralateral SNHL after VS resection, discuss the possible...
Rare Cancers
Fri Mar 06, 2020 22:10
Primary and Recurrent Growing Teratoma Syndrome in Central Nervous System Nongerminomatous Germ Cell Tumors: Case Series and Review of the Literature.
Related ArticlesPrimary and Recurrent Growing Teratoma Syndrome in Central Nervous System Nongerminomatous Germ Cell Tumors: Case Series and Review of the Literature. World Neurosurg. 2020 Feb;134:e360-e371 Authors: Tsuyuguchi S, Sugiyama K, Kinoshita Y, Kolakshyapati M, Takayasu T, Usui S, Takano M, Yonezawa U, Taguchi A, Amatya VJ, Takeshima Y, Kurisu K, Yamasaki F Abstract BACKGROUND: The term "growing teratoma syndrome (GTS)" has been used as follows:...
Rare Cancers
Sat Mar 07, 2020 13:14
Remote Leptomeningeal Dissemination in Olfactory Neuroblastoma Mimicking Multiple Parasagittal Meningiomas: Diagnostic and Therapeutic Challenge.
Related ArticlesRemote Leptomeningeal Dissemination in Olfactory Neuroblastoma Mimicking Multiple Parasagittal Meningiomas: Diagnostic and Therapeutic Challenge. World Neurosurg. 2020 Feb;134:361-364 Authors: Martinez-Perez R, Hardesty DA, Palmer J, Zachariah M, Otto BA, Carrau RL, Prevedello DM Abstract BACKGROUND: Olfactory neuroblastoma (ON) is a highly aggressive and locally recurrent neoplasm. Distant systemic metastases are not uncommon, but remote...
Rare Cancers
Fri Mar 06, 2020 22:10
Intramedullary Spinal Metastatic Renal Cell Carcinoma: Systematic Review of Disease Presentation, Treatment, and Prognosis with Case Illustration.
Related ArticlesIntramedullary Spinal Metastatic Renal Cell Carcinoma: Systematic Review of Disease Presentation, Treatment, and Prognosis with Case Illustration. World Neurosurg. 2020 Feb;134:584-593 Authors: Barrie U, Elguindy M, Pernik M, Adeyemo E, Aoun SG, Hall K, Reyes VP, El Ahmadieh TY, Bagley CA Abstract OBJECTIVE: Renal cell carcinoma (RCC) metastases to the intramedullary spinal cord carry a grim prognosis. The purpose of this review is to...
Rare Cancers
Fri Mar 06, 2020 22:10
Refined Disease Risk Index for Hematological Malignancies, Including Rare Disorders, After Allogeneic Stem Cell Transplantation.
Related ArticlesRefined Disease Risk Index for Hematological Malignancies, Including Rare Disorders, After Allogeneic Stem Cell Transplantation. Transplant Proc. 2019 Dec;51(10):3437-3443 Authors: Fujiwara S, Hattori N, Matsui T, Nakata A, Sasaki Y, Shimada S, Murai S, Abe M, Baba Y, Watanuki M, Kawaguchi Y, Arai N, Kabasawa N, Tsukamoto H, Uto Y, Yanagisawa K, Harada H, Nakamaki T Abstract OBJECTIVE: The refined disease risk index (R-DRI) is a well-designed...
Rare Cancers
Sat Mar 07, 2020 13:14
Sudden Aggravated Radicular Pain Caused by Hemorrhagic Spinal Angiolipomas After Back Massage.
Related ArticlesSudden Aggravated Radicular Pain Caused by Hemorrhagic Spinal Angiolipomas After Back Massage. World Neurosurg. 2020 Feb;134:383-387 Authors: Zhang X, Wang JJ, Guo Y, Dong S, Shi W, Wang G, Zhang H, Wang G Abstract BACKGROUND: Spinal angiolipomas (SALs) are benign tumors that usually present a slow progressive spinal cord or radicular compression. Acute myelopathy or acute aggravated radicular syndrome are exceedingly rare. ...
Rare Cancers
Fri Mar 06, 2020 22:10
Transforaminal Endoscopic Approach for Lumbar Extraforaminal Synovial Cysts: Technical Note.
Related ArticlesTransforaminal Endoscopic Approach for Lumbar Extraforaminal Synovial Cysts: Technical Note. World Neurosurg. 2020 Feb;134:415-419 Authors: Telfeian AE, Oyelese A, Fridley J, Moldovan K, Gokaslan ZL Abstract OBJECTIVE: Lumbar facet cysts are commonly seen in degenerative lumbar conditions causing stenosis and radiculopathy. Extraforaminal lumbar facet cysts are a rare entity and present a surgical challenge because of their location....
Rare Cancers
Sat Mar 07, 2020 13:14
Case of Calcifying Pseudoneoplasms of the Neuraxis Coexisting with Interhemispheric Lipoma and Agenesis of the Corpus Callosum: Involvement of Infiltrating Macrophages.
Related ArticlesCase of Calcifying Pseudoneoplasms of the Neuraxis Coexisting with Interhemispheric Lipoma and Agenesis of the Corpus Callosum: Involvement of Infiltrating Macrophages. World Neurosurg. 2020 Feb;134:635-640.e1 Authors: Inukai M, Shibahara I, Hotta M, Miyasaka K, Sato S, Hide T, Saegusa M, Kumabe T Abstract BACKGROUND: Calcifying pseudoneoplasm of the neuraxis (CAPNON) is a rare clinical entity. We report an unusual case of intraparenchymal...
Rare Cancers
Fri Mar 06, 2020 22:10
Intracranial Inflammatory Pseudotumor Associated with Idiopathic Hypertrophic Pachymeningitis Mimicking Malignant Tumor or High-Grade Meningioma.
Related ArticlesIntracranial Inflammatory Pseudotumor Associated with Idiopathic Hypertrophic Pachymeningitis Mimicking Malignant Tumor or High-Grade Meningioma. World Neurosurg. 2020 Feb;134:372-376 Authors: Han MS, Moon KS, Lee KH, Jang WY, Kim SK, Jung S Abstract BACKGROUND: Idiopathic hypertrophic pachymeningitis (IHP) is a rare clinical disease characterized by inflammatory fibrosis, which causes diffuse thickening of the dura mater. The inflammatory...
Rare Cancers
Sat Mar 07, 2020 13:14
Combined Endoscopic Endonasal and Bilateral Subfrontal Approach for a Nonfunctioning Pituitary Adenoma Associated with an Internal Carotid Artery-Superior Hypophyseal Artery Aneurysm.
Related ArticlesCombined Endoscopic Endonasal and Bilateral Subfrontal Approach for a Nonfunctioning Pituitary Adenoma Associated with an Internal Carotid Artery-Superior Hypophyseal Artery Aneurysm. World Neurosurg. 2020 Feb;134:297-301 Authors: Kino H, Ito Y, Akutsu H, Tanaka S, Hara T, Ishikawa E, Miyamoto H, Matsumaru Y, Matsumura A Abstract BACKGROUND: An aneurysm embedded in a pituitary adenoma is rare, and treatment for both the aneurysm and...
Rare Cancers
Fri Mar 06, 2020 22:10
Facial Nerve Schwannoma Complicated by Acute Hemorrhage After Treatment with Stereotactic Radiosurgery.
Related ArticlesFacial Nerve Schwannoma Complicated by Acute Hemorrhage After Treatment with Stereotactic Radiosurgery. World Neurosurg. 2020 Feb;134:128-132 Authors: Noureldine MHA, Jha RT, Peto I, Malafronte PJ, Allen K, Agazzi S Abstract BACKGROUND: Facial nerve schwannomas (FNSs) are rare benign tumors that arise from Schwann cells of the facial nerve. FNSs are similar to vestibular schwannomas in many aspects, yet their infiltrative nature into...
Rare Cancers
Fri Mar 06, 2020 22:10
Intradural Extramedullary Nonconus Nonfilum Spinal Ependymomas: Report of a Rare Variant and Newer Insights into Their Histogenesis with Proposal of a Classification Scheme and a Management Algorithm Based on a Review of Literature.
Related ArticlesIntradural Extramedullary Nonconus Nonfilum Spinal Ependymomas: Report of a Rare Variant and Newer Insights into Their Histogenesis with Proposal of a Classification Scheme and a Management Algorithm Based on a Review of Literature. World Neurosurg. 2020 Feb;134:323-336 Authors: Das KK, Attri G, Singh S, Bhaisora KS, Verma P, Jaiswal S, Jaiswal A, Behari S Abstract BACKGROUND: Ependymomas are common intramedullary spinal tumors but there...
Rare Cancers
Sat Mar 07, 2020 13:14
A Rapidly Growing Cervical Meningeal Melanocytoma with a Dumbbell-Shaped Extension.
Related ArticlesA Rapidly Growing Cervical Meningeal Melanocytoma with a Dumbbell-Shaped Extension. World Neurosurg. 2020 Feb;134:90-93 Authors: Miura I, Kubota M, Momosaki O, Nyui M, Takebayashi K, Kawamata T, Yuzurihara M Abstract BACKGROUND: Meningeal melanocytoma is a rare benign lesion found in the central nervous system. Preoperative diagnosis of meningeal melanocytoma is often a diagnostic challenge, as the clinical and neurologic features are...
Rare Cancers
Fri Mar 06, 2020 22:10
Acute myeloid leukaemia: recent data on prognostic gene mutations, in relation to stratified therapies for elderly patients.
Related ArticlesAcute myeloid leukaemia: recent data on prognostic gene mutations, in relation to stratified therapies for elderly patients. J BUON. 2019 Jul-Aug;24(4):1326-1339 Authors: Soura EN, Karikas GA Abstract TET2 protein is encoded by the gene TET2 which specifically catalyses the demethylation of 5-methylcytosine to cytosine. Mutations in TET2 have been identified in a number of haematological malignancies, including leukaemias and lymphomas....
Rare Cancers
Fri Mar 06, 2020 22:10
Cerebral Venous Sinus Thrombosis After Transsphenoidal Resection: A Rare Complication of Cushing Disease-Associated Hypercoagulability.
Related ArticlesCerebral Venous Sinus Thrombosis After Transsphenoidal Resection: A Rare Complication of Cushing Disease-Associated Hypercoagulability. World Neurosurg. 2020 Feb;134:86-89 Authors: Soni P, Koech H, Silva D, Das P, Sindwani R, Dobri G, Recinos PF Abstract BACKGROUND: Venous thromboembolism is a well-known complication of Cushing syndrome. Deep vein thrombosis and pulmonary embolic events have been widely reported in patients with Cushing...
Rare Cancers
Fri Mar 06, 2020 22:10
Spontaneous renoalimentary fistula as a complication of upper tract urothelial carcinoma: unknown complication of a rare disease.
Related ArticlesSpontaneous renoalimentary fistula as a complication of upper tract urothelial carcinoma: unknown complication of a rare disease. BMJ Case Rep. 2019 Oct 15;12(10): Authors: Jena R, Sureka SK, Ruidas S, Lal H Abstract Fistulae of the upper urinary tract with the alimentary tract are rare. Most cases of renoalimentary fistulae are secondary to penetrating trauma, which may be iatrogenic or due to locally invasive benign infective processes...
Rare Cancers
Fri Mar 06, 2020 22:10
Thymic Mucoepidermoid Carcinoma: A Systematic Review and Meta-analysis.
Related ArticlesThymic Mucoepidermoid Carcinoma: A Systematic Review and Meta-analysis. Adv Anat Pathol. 2019 Nov;26(6):341-345 Authors: Hamza A, Younes AI, Kalhor N Abstract Thymic mucoepidermoid carcinoma is a rare tumor that remains poorly characterized and a diagnostic challenge. The aim of this review is to characterize this tumor in a larger cohort of patients using all the available cases in the literature. We systematically searched the PubMed...
Rare Cancers
Sat Mar 07, 2020 13:14
Diagnosis of a Rare Intraventricular Schwannoma.
Related ArticlesDiagnosis of a Rare Intraventricular Schwannoma. World Neurosurg. 2020 Feb;134:145-149 Authors: Chiba R, Akiyama Y, Kimura Y, Yokoyama R, Mikuni N Abstract BACKGROUND: Intraventricular schwannoma is extremely rare, with only 35 cases reported to date in the literature. Consequently, its etiology and pathogenesis are still unclear, and therefore require further investigations. Here, we report on and discuss a rare case of intraventricular...
Rare Cancers
Fri Mar 06, 2020 22:10
Primary Mediastinal Nodal and Extranodal Non-Hodgkin Lymphomas: Current Concepts, Historical Evolution, and Useful Diagnostic Approach: Part 1.
Related ArticlesPrimary Mediastinal Nodal and Extranodal Non-Hodgkin Lymphomas: Current Concepts, Historical Evolution, and Useful Diagnostic Approach: Part 1. Adv Anat Pathol. 2019 Nov;26(6):346-370 Authors: Piña-Oviedo S, Moran CA Abstract Primary mediastinal non-Hodgkin lymphomas (PM-NHLs) represent ~5% of all NHLs and comprise lymphomas of B-cell and T-cell origin. PM-NHLs are defined as involvement of mediastinal lymph nodes, thymus, and/or mediastinal...
Rare Cancers
Sat Mar 07, 2020 13:14
Primary Mediastinal Nodal and Extranodal Non-Hodgkin Lymphomas: Current Concepts, Historical Evolution, and Useful Diagnostic Approach: Part 2.
Related ArticlesPrimary Mediastinal Nodal and Extranodal Non-Hodgkin Lymphomas: Current Concepts, Historical Evolution, and Useful Diagnostic Approach: Part 2. Adv Anat Pathol. 2019 Nov;26(6):371-389 Authors: Piña-Oviedo S, Moran CA Abstract Primary mediastinal non-Hodgkin lymphomas (PM-NHLs) represent â¼5% of all non-Hodgkin lymphomas (NHLs) and comprise lymphomas of B-cell and T-cell origin. PM-NHLs are defined as involvement of mediastinal lymph...
Rare Cancers
Sat Mar 07, 2020 13:14
Salivary duct carcinoma: A case report of oncocytic variant with possible treatment implications and review of literature.
Related ArticlesSalivary duct carcinoma: A case report of oncocytic variant with possible treatment implications and review of literature. Pathol Res Pract. 2019 Oct;215(10):152549 Authors: Sekhri R, Ortanca I, Boals C, Agarwal S Abstract Salivary duct carcinoma (SDC) is an aggressive malignancy, resembling high-grade ductal carcinoma of the breast. Histologically, it shows cords and nests with cribriforming, marked nuclear atypia, comedonecrosis, perineural,...
Rare Cancers
Fri Mar 06, 2020 22:10
Follicular dendritic cell sarcoma (FDCS) of urinary bladder with coexisting urothelial carcinoma-a case report.
Related ArticlesFollicular dendritic cell sarcoma (FDCS) of urinary bladder with coexisting urothelial carcinoma-a case report. BMC Urol. 2019 Sep 05;19(1):83 Authors: Sun J, Wang C, Wang D, Wu J, Wang L, Zhao L, Teng L Abstract BACKGROUND: Follicular dendritic cell sarcoma is a very rare bladder tumor with very few cases that have been reported in the English literature. CASE PRESENTATION: We report an unusual case of follicular dendritic...
Rare Cancers
Fri Mar 06, 2020 22:10
An Adrenal Hepatoid Adenocarcinoma with Left Renal Vein Thrombosis Extending into the Inferior Vena Cava.
Related ArticlesAn Adrenal Hepatoid Adenocarcinoma with Left Renal Vein Thrombosis Extending into the Inferior Vena Cava. Urol J. 2019 Oct 21;16(5):511-514 Authors: Deng X, Jin Y, Yang W, Wang S, Mu H, Yu K, He Y Abstract Hepatoid adenocarcinoma (HAC) is an uncommon tumor with morphological resemblance to hepatocellular car-cinoma. HAC of the adrenal glands is extremely rare. Here, we report the case of an 83-year-old man with adrenal HAC who presented...
Rare Cancers
Fri Mar 06, 2020 22:10
Complete excision of esophageal bronchogenic cyst by endoscopic submucosal tunnel dissection: a case presentation.
Related ArticlesComplete excision of esophageal bronchogenic cyst by endoscopic submucosal tunnel dissection: a case presentation. BMC Gastroenterol. 2019 Aug 28;19(1):155 Authors: Yang X, Zong Y, Zhao HY, Wu YD, Ji M Abstract BACKGROUND: Intramural esophageal bronchogenic cyst is very rare. Surgical removal of the cysts is advised even the patients are asymptomatic, since the cyst can lead to complications, and there is a risk of malignant transformation....
Rare Cancers
Fri Mar 06, 2020 22:10
Rare case of an upper urinary tract carcinoma (UTUC) in renal pelvis and ureter associated to renal vein thrombosis: diagnostic imaging with CECT, MRI and CEUS.
Related ArticlesRare case of an upper urinary tract carcinoma (UTUC) in renal pelvis and ureter associated to renal vein thrombosis: diagnostic imaging with CECT, MRI and CEUS. J Ultrasound. 2019 Sep;22(3):373-379 Authors: Matteo M, Elena B, Cristina BM, Ginevra D, Costanza V, Simone A, Vittorio M Abstract A 58-year-old woman complaining of dyspnea and mild flank pain was admitted to our radiology department after undergoing ultrasonography in another...
Rare Cancers
Fri Mar 06, 2020 22:10
Multifocal Gastrointestinal Melanoma.
Related ArticlesMultifocal Gastrointestinal Melanoma. J Gastrointestin Liver Dis. 2019 Jun 01;28:237-240 Authors: Kouvaras S, Rokkas T, Goga H, Gakiopoulou H, Arapantoni P, Haliotis G, Mantas D Abstract Primary mucosal melanoma is a rare disease, with a worse prognosis than cutaneous melanoma. We present a patient with primary melanoma of the stomach and small intestine, with good outcome after radical surgical excision and adjuvant ipilimumab therapy.PMID:...
Rare Cancers
Fri Mar 06, 2020 22:10
[Therapeutic failure in skin carcinomas of the face].
Related Articles[Therapeutic failure in skin carcinomas of the face]. Ann Chir Plast Esthet. 2019 Nov;64(5-6):552-560 Authors: Barthelemy I Abstract Therapeutic failures in the management of skin carcinomas of the face are not rare, because of the very high frequency of these lesions. They come in 3 aspects: (a) tumor recurrence at the site of resection: reminders concerning the margins of excision in first surgery and in case of recurrence are made,...
Rare Cancers
Fri Mar 06, 2020 22:10
Thoracic Hyper-IgG4-Related Disease Mimicking Malignant Pleural Mesothelioma.
Related ArticlesThoracic Hyper-IgG4-Related Disease Mimicking Malignant Pleural Mesothelioma. Lung. 2019 06;197(3):387-390 Authors: Lococo F, Di Stefano T, Rapicetta C, Piro R, Gelli MC, Muratore F, Ricchetti T, Taddei S, Zizzo M, Cesario A, Facciolongo N, Paci M Abstract We report a rare case of a IgG4-related disease presenting with recurrent pleural effusion, pleural thickness and multiple mediastinal lymphadenopathies and no involvement of other...
Rare Cancers
Sat Mar 07, 2020 13:14
Prevalence and prognostic value of PD-L1 expression in molecular subtypes of metastatic large cell neuroendocrine carcinoma (LCNEC).
Related ArticlesPrevalence and prognostic value of PD-L1 expression in molecular subtypes of metastatic large cell neuroendocrine carcinoma (LCNEC). Lung Cancer. 2019 04;130:179-186 Authors: Hermans BCM, Derks JL, Thunnissen E, van Suylen RJ, den Bakker MA, Groen HJM, Smit EF, Damhuis RA, van den Broek EC, Stallinga CM, Roemen GM, Speel EJM, Dingemans AC, PALGA-group Abstract BACKGROUND: Pulmonary large cell neuroendocrine carcinoma (LCNEC) is a rare...
Rare Cancers
Sat Mar 07, 2020 13:14

Cellular Origin, Tumor Progression, and Pathogenic Mechanisms of Cutaneous Neurofibromas Revealed by Mice with Nf1 Knockout in Boundary Cap Cells.
Related ArticlesCellular Origin, Tumor Progression, and Pathogenic Mechanisms of Cutaneous Neurofibromas Revealed by Mice with Nf1 Knockout in Boundary Cap Cells. Cancer Discov. 2019 01;9(1):130-147 Authors: Radomska KJ, Coulpier F, Gresset A, Schmitt A, Debbiche A, Lemoine S, Wolkenstein P, Vallat JM, Charnay P, Topilko P Abstract Patients carrying an inactive NF1 allele develop tumors of Schwann cell origin called neurofibromas (NF). Genetically engineered...
Rare Cancers
Fri Mar 06, 2020 22:10
Identification of Leptomeningeal Medulloblastoma with Contrast-Enhanced Magnetic Resonance Imaging: A Devastating Differential of Acute Disseminated Encephomyelitis.
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Fri Mar 06, 2020 22:10

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